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Is there a poison that smells like maple syrup?
Sotolon (also known as sotolone) is a lactone and an extremely powerful aroma compound, with the typical smell of fenugreek or curry at high concentrations and maple syrup, caramel, or burnt sugar at lower concentrations….Sotolon.
| Names | |
|---|---|
| PubChem CID | 62835 |
| UNII | T62RL2NEGW |
| CompTox Dashboard ( EPA ) | DTXSID4047674 |
| show InChI |
Why does my breath smell like maple syrup?
Breath that smells like maple syrup The inability to metabolize three types of amino acids (leucine, isoleucine, and valine) can cause maple syrup urine disease, in which a person’s breath or urine smell like maple syrup or caramelized sugar.
What are the symptoms of maple syrup urine disease?
The condition gets its name from the distinctive sweet odor of affected infants’ urine. It is also characterized by poor feeding, vomiting, lack of energy (lethargy), abnormal movements, and delayed development. If untreated, maple syrup urine disease can lead to seizures, coma, and death.
Can adults get maple syrup urine disease?
People with MSUD can grow into adulthood by following a strict diet and avoiding illness and stress as much as they can. While it is possible to manage the disorder with a protein-restricted diet and close medical supervision, people with MSUD are always at risk of having a metabolic attack.
What is the life expectancy of someone with maple syrup urine disease?
Maple syrup urine disease (MSUD) type 1B is an inherited metabolic disorder named for the characteristic maple syrup smell of the affected person’s urine. If carefully treated with a low-protein diet, people with MSUD can live fairly normal lives.
What is maple syrup disease?
Maple syrup urine disease (MSUD) is a rare metabolic disorder that some babies are born with. It’s caused by a defect in the enzymes that break down some amino acids. Most newborn babies in the United States have their blood tested for MSUD as part of newborn screening.
What is Hartnups disease?
Hartnup disease is a condition caused by the body’s inability to absorb certain protein building blocks (amino acids) from the diet. As a result, affected individuals are not able to use these amino acids to produce other substances, such as vitamins and proteins.
Can maple syrup disease go undetected?
While newborn screening programs allow for early detection of classic MSUD, cases of the intermittent form might go undetected, and present later in childhood following metabolic derailment, with an array of non-specific symptoms.
Why does my kid always smell like syrup?
WHAT IS MSUD? MSUD stands for “maple syrup urine disease.” It is named for the sweet maple syrup smell of the urine in untreated babies. This condition is one type of amino acid disorder. People with MSUD have problems breaking down certain amino acids found in protein.
Can maple syrup urine disease go undetected?